Cystic fibrosis
In cystic fibrosis, particularly severe mucus is formed in all exocrine glands as a result of a genetic defect. Cystic fibrosis should be kept in mind given meconium ileus, recurrent or chronic bronchitis, chronic failure to thrive, recurrent nasal polyps, cloudy liver problems, and male infertility. The disease is not yet curable. The survival rate is increasing continuously and is now approximately 40 years. Children and adults are supported on an interdisciplinary basis. A newborn screening for cystic fibrosis is performed in Germany to detect the disease as early as possible.
Treatment / Therapy
DIAGNOSTICS
- Medical history and clinical examination
- Sweat test
- Genomic diagnostics
- Functional diagnostics (such as lung function, including bodyplethysmography, ergospirometry, and diffusion; sonography, other imaging diagnostics)
THERAPY FORMS
- Outpatient therapy (regular 4x annual visit)
- Inpatient therapybr />
- In the event of exacerbations, over 10-14 days
- as intermittent intravenous antibiotic therapy 4x annually over 10-14 days with pseudomonas colonisation
- initiation of home parenteral intravenous antibiotic therapy (beginning at 4 days in a hospital, continuation at home for 10 days with care by specialised nurses, suitable for working adults)
CERTIFICATION
The Greifswald outpatient service is certified as part of the Mukoviszidose-Zentrum Mecklenburg-Vorpommern, by the medical chamber, and by the Mukoviszidose eV for the treatment of cystic fibrosis in children and adults.
Contact
Clinic and Polyclinic for Children and Adolescent Medicine
PD Dr. Sebastian Schmidt
Clinic and Polyclinic for Children and Adolescent Medicine
PD Dr. Roswitha Bruns
Contact
Tamara Usichenko
Geschäftsbereich Patientenmanagement
Universitätsmedizin Greifswald
Fleischmannstr. 8
17475 Greifswald
Phone: +49 3834 86-5184
Mobil: +49 151 55459980
E-Mail: international.patientsmed.uni-greifswaldde